Fibulins: physiological and disease perspectives.

نویسندگان

  • W Scott Argraves
  • Lisa M Greene
  • Marion A Cooley
  • William M Gallagher
چکیده

The fibulins are a family of proteins that are associated with basement membranes and elastic extracellular matrix fibres. This review summarizes findings from studies of animal models of fibulin deficiency, human fibulin gene mutations, human tumours and injury models that have advanced our understanding of the normal and pathological roles of members of this formerly obscure family.

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عنوان ژورنال:
  • EMBO reports

دوره 4 12  شماره 

صفحات  -

تاریخ انتشار 2003